Learn more about our Research & Clinical Trials
Referring Providers: Register for our next CE Symposium
At the same time, it completely depends on the presence or absence of concomitant developmental anomalies, chromosomal abnormalities and the time period for diagnosing the pathology. Statistics show that postnatal morbidity in children, as well as the postnatal mortality rate, is an order of magnitude higher in cases where the syndrome is diagnosed in the prenatal period, and not in the neonatal period. For a patient, Dandy-Walker syndrome can be fraught with mental and mental defects for life, delayed psychomotor development, lifelong preservation of neurological pathologies (increased muscle tone, impaired coordination of movements, etc.). In addition, it is worth noting that this disease has a very high risk of death.
Treatment of the Dandy-Walker syndrome. Treatment of Dandy-Walker syndrome is carried out exclusively by surgery. During the operation, a shunt is placed in the patient's fourth ventricle to ensure that it communicates with the abdominal cavity. The shunting method allows you to remove excess cerebrospinal fluid and reduce intracranial pressure. The possibility of treating Dandy-Walker syndrome. Dandy-Walker syndrome is a rare congenital anomaly that women are more susceptible to. The frequency of the birth of children with such a pathology is one case per 25 thousand newborns.
In babies, deviations in the structure and development of the cerebellum and the pathways involved in the outflow of cerebrospinal fluid are diagnosed. The syndrome is often determined in the prenatal period, usually manifests itself immediately at birth, less often - at the age of up to a year.
Pathology is named after the scientists who first described it. American-born physician Walter Edward Dandy, who is considered one of the founders of neurosurgery, first described the disease in 1921. His writings were supplemented by the research of Earl Walker.
Anomaly in the structure of the cerebellum. hypertrophy of the hemispheres and a decrease or complete absence of the worm between them. Pathological enlargement of the fourth ventricle - a hollow formation in which cerebrospinal fluid accumulates. Overgrowth or absence of pathways that produce an outflow of cerebrospinal fluid. The presence of a hollow tumor in the posterior cranial fossa.
Provoking factors Main signs Possible complications and prognosis Researches required Treatment options Operation Drugs Prevention. The disease is manifested by the following features. All these phenomena entail intracranial hypertension, hydrocephalus, which affects the functioning of not only the organ itself, but also the work of other body systems.
Infections transferred in the prenatal period, in particular, herpes, rubella, CMVI. Such diseases are considered dangerous for the fetus during the first 14 weeks of pregnancy. Maternal autoimmune disease. exchange violations. Dependence on toxic substances (alcohol, smoking, drugs) during gestation.
An anomaly refers to hereditary diseases with an undetermined cause. The circumstances that provoke the development of Dandy-Walker syndrome in children are. These circumstances lead to the fact that in the prenatal period the cerebellum, ventricles and cerebrospinal fluid channels are not properly formed in the fetus, which leads to multiple deviations in the functioning of other organs.
The disease is classified according to the principle of the degree of insufficiency in the development of cerebellar structures. Based on this, complete and incomplete forms of the disease are distinguished. The manifestations of the disease in newborns and in adult children are different. The specialist can see the first signs on ultrasound even in the prenatal period, these include.
